Cardiac involvement in Erdheim-Chester disease: a case report.

Autores

  • Fernando Pivatto Júnior Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil
  • Diogo Silva Piardi Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil
  • Felipe Soares Torres Radiology Department, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil

Palavras-chave:

Erdheim-Chester disease, heart failure, magnetic resonance imaging

Resumo

Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis of unknown etiology characterized by proliferation of lipid-containing foamy histiocytes affecting bones and potentially every organ. There is a wide clinical spectrum of the disease, ranging from asymptomatic bone or soft-tissue lesions to life-threatening systemic involvement. Although the initial descriptions published by Jakob Erdheim and William Chester in 1930 included a patient with right atrial infiltration on autopsy, cardiovascular involvement in ECD has only gained more recognition recently. In the present report, we describe a case with cardiac involvement, presenting with symptomatic heart failure and a cardiac mass assessed with echocardiogram and cardiac magnetic resonance imaging.

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Publicado

2015-01-16

Como Citar

1.
Pivatto Júnior F, Piardi DS, Torres FS. Cardiac involvement in Erdheim-Chester disease: a case report. Clin Biomed Res [Internet]. 16º de janeiro de 2015 [citado 2º de dezembro de 2022];34(4). Disponível em: https://seer.ufrgs.br/index.php/hcpa/article/view/51436

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