Giant Lipofibromatous Hamartoma of Median Nerve in a Child

Authors

  • Ricardo Vieira Teles-Filho Departamento de Radiologia e Diagnóstico por Imagem, Faculdade de Medicina, Universidade Federal de Goiás, Goiânia - GO, Brasil.
  • Guilherme de Matos Abe Departamento de Radiologia e Diagnóstico por Imagem, Faculdade de Medicina, Universidade Federal de Goiás. Goiânia, GO, Brasil.
  • Paulo Henrique de Aquino Júnior Faculdade de Medicina, Universidade Federal de Goiás. Goiânia, GO, Brasil.
  • Giovanni Ferreira Viggiano Departamento de Radiologia e Diagnóstico por Imagem, Faculdade de Medicina, Universidade Federal de Goiás. Goiânia, GO, Brasil. https://orcid.org/0000-0003-2623-4342
  • Bruna Ribas Teixeira Departamento de Radiologia e Diagnóstico por Imagem, Faculdade de Medicina, Universidade Federal de Goiás. Goiânia, GO, Brasil.
  • Murilo Eugênio Oliveira Departamento de Radiologia e Diagnóstico por Imagem, Faculdade de Medicina, Universidade Federal de Goiás. Goiânia, GO, Brasil.

Keywords:

Lipofibromatous hamartoma, Median nerve, Magnetic resonance imaging

Abstract

Lipofibromatous hamartoma (LFH) is a rare fibrofatty tumor of adipocytes within peripheral nerves, affecting mainly children. It typically presents as a palpable mass surrounding the nerves of the upper limbs, causing pain and neurological deficits in the affected nerve distribution. We report the case of a child with a 2-years presentation of a mass in the right wrist associated with pain and paresthesia, who underwent investigation with magnetic resonance imaging (MR I). It showed thickening of the median nerve with spaghetti-like appearance associated with lipomatous tissue in a coaxial cable-like pattern, both features characteristic of LFH. This case illustrates the importance of MRI in the differential diagnosis of limb masses in the pediatric population.

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Published

2023-05-29

How to Cite

1.
Vieira Teles-Filho R, de Matos Abe G, de Aquino Júnior PH, Ferreira Viggiano G, Ribas Teixeira B, Eugênio Oliveira M. Giant Lipofibromatous Hamartoma of Median Nerve in a Child. Clin Biomed Res [Internet]. 2023 May 29 [cited 2025 May 2];43(1). Available from: https://seer.ufrgs.br/index.php/hcpa/article/view/125914

Issue

Vol. 43 No. 1 (2023): Clinical and Biomedical Research

Section

Case Report

License

Copyright (c) 2023 RICARDO VIEIRA TELES FILHO, Guilherme de Matos Abe, Paulo Henrique de Aquino Júnior, Giovanni Ferreira Viggiano, Bruna Ribas Teixeira, Murilo Eugênio Oliveira

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