Nutritional status in patients attended at an adult program for cystic fibrosis patients

Bruna Ziegler, Paula Maria Eidt Rovedder, Claudine Lacerda Oliveira, Paulo de Tarso Roth Dalcin, Janice Luisa Lukrafka


Introduction: In cystic fibrosis (CF) nutritional status is associated with growth, lung function and survival rates. Objective: To evaluated the nutritional status in adults with CF and correlating with clinical score, chest radiographic score, maximal respiratory pres-sures, submaximal exercise capacity and pulmonary function. Methods: This was a prospective cross-sectional study in patients (16 years and older) attending to an adult CF program. The patients were submitted to a clinical and nutritional evaluation, six minute walk test (6MWT), maximal respiratory pressures, spirometry and chest roentgenograms. Results: The study included 41 patients with a mean age of 23.7 ± 6.5 years and a mean body mass index (BMI) of 20.2 ± 2.2 Kg/m2. Twenty six patients (63.4%) were classified as well nourished (BMI = 21.7 ± 2.0 Kg/m2), six (14.6%) were at nutritional risk (BMI = 19.4 ± 0.50 Kg/m2) and 9 (22%) were malnourished (BMI = 17.6 ± 0.8 Kg/m2). There were no significant correlation between BMI and age (r = 0.24; P = 0.13), age at diagnosis (r = -0.04; P = 0.81), clinical (r = 0.13; P = 0.40) and radiographic (r = -0.22; P = 0.17) scores, distance walked in 6MWT (r = 0.20; P = 0.20), FEV1 % (r = 0.11; P = 0.50) and FVC % (r = 0.06; P = 0.72). Also, there were no significant association between the decline of nutritional status and these variables. Conclusion: This study showed that the majority of patients with CF (16 years and older) have an adequate nutritional status (63.4%), but a significant percentage (36.6%) have a nutritional depletion. There was no significant association between nutritional status and pulmonary function, maximal respiratory pressures, clinical and chest radiographic score and submaximal exercise capacity.
Keywords: Cystic fibrosis, nutritional status, pulmonary function, adults, submaximal exercise capacity.


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ISSN: 2357-9730



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